The cystic dilatation of the lower part of the ureter is known as ureterocoele which has been associated with other anomalies such as stenotic ureteric orifice, duplicated urinary system, and hydronephrosis along with or without other clinical sequelae. Notably, the accurate and prompt diagnosis is challenging due to non-specific symptoms that could mimic other urogenital systems diseases. Imaging evaluation is the gold standard of accurate diagnosis and comprehensive clinical examination.The possible complications associated with ureterocoele include urinary tract obstruction, reflux, continence, and renal function derangements. Thus, we present a 23-year-old male patient, who presented to the general outpatient clinic of the Federal Teaching Hospital, Abakaliki, in September 2018 with a complaint of right-sidedabdominal pain and hot sensation, intermittent haematuria, and pain during micturition of one-year duration. He was evaluated with ultrasonography that showed moderate right hydronephrosis with a large curvilinear calculus adjacent to the dilated ureteric end, and intravenous urography revealed a dilated right distal ureteric end with a peripheral halo, giving the cobra head the appearance of ureterocoele.The patient underwent open cystolithotomy with marsupialization of the distal end of the right ureter. He showed remarkable post-operative improvement and was discharged after two weeks. Two months of post-operative follow-up was uneventful.

KEYWORDS: Ureterocoele, Cystolithiasis, Ultrasonography, Intravenous urography